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alopecias table

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Introduction

The tables below records disorders known to involve alopecia. The first table lists disorders where alopecia is a primary symptom. The second table lists disorders where alopecia can be one of several symptoms. Typically the other symptoms are of greater concern and health or life threatening.

The clinical distinction between alopecia and hypotrichosis is that alopecia involves hair growth that is later lost. Hypotrichosis is a lack of any hair growth. The distinction between alopecia and hypotrichosis is not clear cut for many disorders. Some dermatologists will disagree with my listing. You may find some disorders in both the alopecia and hypotrichosis listings. This is not necessarily a complete list of disorders involving alopecia. Links to relevant web pages on the Online Mendelian Inheritance in Man (OMIM) web database are given where possible.

Where a disorder is known by more than one name, alternative names are given in the second column and the record duplicated in the first column under each respective name. Brackets around alternative disorder names indicate an indirect association, for example a subcategory of the disorder. These records are not duplicated in the first column.


List of disorders involving hair loss (alopecias) as a primary symptom

Disorders with alopecia as a primary symptom Alternative names for disorder Links to OMIM web pages for disorder (where available)
     
Alopecia areata (Alopecia totalis,
Alopecia universalis)
104000
Alopecia cicatrisata Pseudopelade of Brocq
(Pseudopelade)
 
Alopecia totalis Alopecia areata 104000
Alopecia universalis Alopecia areata 104000
Alopecia keratosis pilaris    
Alopecia triangularis    
Anagen effluvium    
Androgeneic alopecia (Pattern baldness) 109200
Androgenetic alopecia (Pattern baldness) 109200
Area celsi Alopecia areata 104000
Bacterial follicultiis    
Black piedra    
Blackdot ringworm    
Cemical alopecia (Necrotic alopecia)  
Cicatrical alopecia    
Chronic telogen effluvium    
Dermatophyte infection    
Diet deficiency induced alopecia (Telogen effluvium)  
Diffuse alopecia    
Dissecting cellulitis Perifolliculitis capitis abscedens et suffodiens (Hoffman)
(Dissecting folliculitis)
260910
Drug induced alopecia (Telogen effluvium)  
Eosinophilic pustular folliculitis Ofuji syndrome  
Erosive pustular dermatosis Folliculitis decalvans  
Familial focal alopecia   104110
Feldman syndrome    
Female pattern baldness (Pattern baldness) 109200
Follicular degeneration syndrome Hot comb alopecia  
Folliculitis barbae    
Folliculitis decalvans Erosive pustular dermatosis (Folliculite epilante,
Folliculitis depilans)
 
Folliculitis keloidalis (Acne keloidalis nuchae,
dermatitis papillaris capillitii)
 
Graham-Little syndrome    
Herpes simplex folliculitis    
Herpes zoster folliculitis    
Hot comb alopecia Follicular degeneration syndrome  
Involutional alopecia (Senescent alopecia,
Senile alopecia)
 
Ischemic alopecia (Pressure alopecia,
Vasoconstriction alopecia)
 
Keratosis follicularis spinulosa decalvans cum ophiasi   308800
Lichen planopilaris (Lichen planus)  
Lipedematous alopecia    
Loose anagen syndrome Loose hair syndrome
(Loose anagen hair)
600628
Loose hair syndrome Loose anagen syndrome
(Loose anagen hair)
600628
Male pattern baldness Androgenetic alopecia
(Pattern baldness)
109200
Mechanically induced alopecia Traction alopecia  
Mixed inflammatory alopecia    
Occipital alopecia (Physiological)  
Occipital alopecia areata Alopecia areata 104000
Ofuji syndrome Eosinophilic pustular folliculitis  
Papular atrichia Congenital atrichia? 209500
203655
Pattern Baldness Androgenetic alopecia 109200
Perifolliculitis capitis abscedens et suffodiens of Hoffman Dissecting cellulitis
(Dissecting folliculitis)
 
Perinevoid alopecia areata   104000
Postpartum alopecia (Telogen effluvium)  
Pseudofolliculitis barbae    
Pseudopelade of Brocq Alopecia cicatrisata
(Pseudopelade)
 
Ringworm Tinea capitis  
Sarcoidosis    
Scarring alopecia Cicatrical alopecia
Permanent alopecia
 
Telogen effluvium    
Thermal alopecia (Necrotic alopecia)  
Tick bite induced alopecia    
Tinea capitis Ringworm  
Traction alopecia Mechanically induced alopecia  
Traction folliculitis    
Traumatic alopecia (Necrotic alopecia)  
Triangular alopecia    
Trichomycosis axillaris    
Trichotillomania    
Tufted hair folliculitis    
Vaccination induced alopecia (Telogen effluvium?)  


List of disorders involving hair loss (alopecias) as a secondary symptom

Disorders with alopecia as a secondary symptom Alternative names for disorder Links to OMIM web pages for disorder (where available)
     
Acrodermatitis enteropathica Zinc deficiency 201100
Alopecia mucinosa    
Alopecia-epilepsy-oligophrenia syndrome of Moynahan Moynahan syndrome 203600
Alopecia ichthyotica (Congenital ichthyosis) 242300
Aminoacidurias    
Amyloidosis   105250
301220
Anemia (Various) List
Angiosarcoma    
Alopecia congenita with keratosis palmoplantaris   104100
Aplasia cutis congenita (Congenital defects of skull and scalp) 107600
107601
207731
600360
601075
Atrophodermia vermiculata Folliculitis ulerythematosa,
Hot comb atrophy,
Atrophodermia reticulata
209700
Bacterial folliculitis    
Baraitser syndrome    
Basel cell carcinoma    
Bazex syndrome Follicular atrophoderma and basel cell carcinoma syndrome,
Bazex-Dupre-Christol syndrome
301845
Bazex-Dupre-Christol syndrome Follicular atrophoderma and basel cell carcinoma syndrome,
Bazex syndrome
301845
Biotin (vitamin B complex) deficiency Biotin responsive disorder  
Biotinidase deficiency Biotin responsive disorder, Multiple carboxylase deficiency 253260
Bloch-Sulzberger syndrome Incontinentia pigmenti type I 308300
Cancer (Various) List
Cantu syndrome   114620
Carcinoma (Various) List
Chemotherapy    
Cicatrical pemphigoid    
Congenital Hemidysplasia with Ichthyosiform erythroderma and Limb Defects (CHILD) syndrome   308050
Congenital atrichia (Papular atrichia?) 203655
209500
Crohn disease (Inflammatory bowel disease) 266600
Cronkite-Canada syndrome    
Darier disease Keratosis follicularis 124200
Diabetes (Various) List
Dialysis induced alopecia    
Discoid lupus erythematosus    
Dissecting folliculitis Perifolliculitis capitis abscedens et suffodiens (Hoffman)  
Down syndrome (Trisomy 21) 190685
Eosinophilia-myalgia syndrome   131400
Epidermolysis bullosa acquisita    
Epidermolysis bullosa    
Erosive pustular dermatosis    
Erythrokeratoderma variabilis Greither syndrome 133200
Favus    
Fibrodysplasia ossificans progressiva   135100
Follicular atrophoderma and basel cell carcinoma syndrome Bazex-Dupre-Christol syndrome,
Bazex syndrome
301845
Follicular occulsion triad    
Follicular degeneration syndrome    
Follicular hyperkeratosis    
Folliculitis keloidalis    
Glucagonoma syndrome    
Greither syndrome Erythrokeratoderma variabilis 133200
Hallerman-Streiff syndrome    
Hamartomas    
Hartnup disease   234500
Hemifacial atrophy, progressive Parry-Romberg syndrome 141300
Hemochromatosis   235200
602390
Hidradenitis suppurativa   142690
Hodgkin disease   236000
Holocarboxylase deficiency Biotin deficiency,
Multiple synthetase carboxylase deficiency
253270
Homocystinuria   236200
Hypersensitivity disorders (Various) List
Hypomelanosis of Ito Incontinentia pigmenti achromians 146150
Ichthyosis follicularis    
Incontinentia pigmenti type I Bloch-Sulzberger syndrome 308300
Incontinentia pigmenti type II   308310
Incontinentia pigmenti achromians Hypomelanosis of Ito 146150
Inflammatory bowel disease   601458
191390
266600
Insect bites    
Keratosis follicularis Darier disease 124200
Keloidal folliculitis    
Keratosis pilaris    
Keratosis pilaris atrophicans    
Keratosis pilaris decalvans    
Keratosis follicularis    
Kerion (Various) List
Kinky hair syndrome Menkes syndrome,
Steely hair disease
(copper transport disease)
309400
Kwashiorkor    
Leishmaniasis    
Leukemia (Various) List
Linear sebaceous nevus syndrome Nevus sebaceus of Jadassohn 163200
Lipedematous alopecia    
Lipoid proteinosis    
Lupus erthyematosus   152700
Lymphoma (Various) List
Lymphoproliferative disorders   601859
Malnutrition    
Menkes syndrome Kinky hair syndrome,
Steely hair disease
(copper transport disease)
309400
Metastatic diseases (Various) List
Mineral deficiencies    
Morphea    
Moth eaten alopecia Syphilis  
Moynahan syndrome Alopecia-epilepsy-oligophrenia syndrome of Moynahan 203600
Multiple carboxylase deficiency Biotin responsive disorder,
Biotinidase deficiency
253260
Multiple synthetase carboxylase deficiency Biotin deficiency,
Holocarboxylase deficiency
253270
Multiple sclerosis   126200
Mycosis fungoides   254400
Myositis ossificans progressiva    
Neoplasm (Various) List
Nevi (Various) List
Nevus sebaceus of Jadassohn Linear sebaceous nevus syndrome 163200
Olmstead syndrome    
Pachyonychia congenita   167200
167210
Palmoplantar hyperkeratosis (Various) List
Parry-Romberg syndrome Hemifacial atrophy, progressive 141300
Perifolliculitis capitis abscedens et suffodiens (Hoffman) Dissecting folliculitis  
Physiological stress    
Pink disease    
Pityriasis amiantacea    
Poikiloderma atrophicans and cataract Rothmund-Thomson syndrome 268400
Poland anomaly   173800
Polycystic ovary syndrome Stein-Leventhal syndrome 184700
Polyglandular autoimmune syndrome   269200
240300
Porokeratosis of Mibelli   175800
Porphyria   176000
176010
176090
176100
176200
263700
Postpartum alopecia    
Pregnancy    
Premature senility    
Pressure injury    
Progeria   176670
Protein malnutrition    
Pseudofolliculitis barbae    
Psoriasis   177900
601454
602723
Radiation induced alopecia    
Ringworm Tinea capitis  
Rothmund-Thomson syndrome Poikiloderma atrophicans and cataract 268400
Scleroderma   181750
Seborrheic dermatitis    
Secondary syphilis    
Severe Combined Immunodeficiency (SCID)   202500
312863
600802
601457
602450
Sezary syndrome    
Sheehan syndrome    
Sicca syndrome Sjogren syndrome 270150
Sjogren syndrome Sicca syndrome 270150
Squamous cell carcinoma    
Steely hair disease Menkes syndrome,
Kinky hair syndrome
(Copper transport disease)
309400
Stein-Leventhal syndrome Polycystic ovary syndrome 184700
Stress    
Syphilis Moth eaten alopecia  
Syringolymphoid hyperplasia    
Syringoma   186600
Systemic lupus erythematosus   152700
Thyroid disorders (Various) List
Tinea capitis Ringworm  
Trauma    
Traumatic alopecia    
Treacher-Collins syndrome Mandibulofacial dystosis 154500
Trichomalacia    
Tuberculoid leprosy   246300
Tuberculosis    
Ulcerative colitis (Inflammatory bowel disease) 191390
Ulerythema ophryogenes    
Vitamin deficiencies    
Vitiligo   193200
Vogt-Koyanagi-Harada syndrome    
Vohwinkel syndrome   193200
Weight loss    
Zinc deficiency Acrodermatitis enteropathica 201100

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